ECG FEATURES REMAIN IN YOUNG PEOPLE WITH MARFANOID HABITUS

Abstract

According to the Russian recommendations on hereditary connective tissue disorders, it was proposed to isolate a number of dysplastic phenotypes, the most common and studied is marfanoid habitus (MH). It has been established that patients with MH develop remodeling of the heart and aorta, clinically significant cardiac arrhythmias. Characteristics of the atrioventricular complex in patients with MH have not been previously evaluated. Materials and methods. We surveyed 92 young men (average age 20.7±0.6 years). Were performed anthropometric and phenotypic examinations, as rest ECG recording for 24 s in 12 standard leads. Results. Young people with MH are characterized by a longer duration of the atrioventricular delay and more frequent detection of episodes of ectopic atrial pace and migration of the supraventricular pacemaker. Pronounced dysaxia (discrepancy of depolarization vectors in repolarization of more than 60º) was detected mainly in young men with MH and was practically not registered in the control group. Conclusion. The resting ECG does not allow to establish the essential features of the atrioventricular complex in young people with MH. A third of young men with MH show a significant discrepancy in the directions of depolarization and repolarization processes, which may complicate the assessment of violations of repolarization processes.