CAKUT SYNDROME IN CHILDREN WITH MANIFESTATIONS OF CONNECTIVE TISSUE DYSPLASIA (CLINICAL CASE)

Abstract

Congenital anomalies of the kidneys and urinary tract in children are the cause of chronic renal failure in 65% of cases. Hypoplastic renal dysplasia accounts for 2.7% of all malformations of the urinary system. All patients with malformations of the urinary system have external and/or visceral symptoms of connective tissue dysplasia of various organs and systems. The prevalence of pathology of the urinary system against the background of connective tissue dysplasia reaches 68-80%. The article presents a clinical case of a patient who was hospitalized in our clinic with hypoplastic dysplasia of the right kidney, complicated by chronic pyelonephritis and secondary arterial hypertension. Dysplasia of connective tissue with multiple organ changes was a background contributing to the development of complications in this patient.