WILKIE SYNDROME AS A COMPLICATION OF MISDIAGNOSED CROHN’S DISEASE
Abstract
Wilkie’s syndrome or superior mesenteric artery (SMA) syndrome is a relatively rare condition due to abnormal branching of the SMA from the abdominal aorta due to the disappearance of adipose tissue that provides stability of the angle between the two major arterial vessels and, consequently, compression of the duodenum with subsequent impaired passage. The development of Wilkie’s syndrome, given the data of the literature and our own experience, is always secondary. The peculiarity of our clinical case of Wilkie’s syndrome in an adolescent girl is the child’s prolonged treatment for misdiagnosed Crohn’s disease of the colon, followed by the discovery of angiodysplasia and repeated surgical interventions, resulting in weight loss and, consequently, the development of syndrome or SMA.
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