A CLINICAL CASE OF EOSINOPHILIC GRANULOMATOSIS WITH POLYANGIITIS COMPLICATED BY LUNG, HEART AND GASTROINTESTINAL TRACT DAMAGE
Abstract
Eosinophilic granulomatosis with polyangiitis (EGP), also referred to as Churge-Strauss syndrome, is a rare immune–mediated disease. According to the results of a meta-analysis from 2021, the prevalence of the described nosology is 1.22 per 1,000,000 population. Currently, the disease is classified according to the nomenclature of vasculitis, adopted at the 2012 conference in the same Chapel Hill, according to which the division occurs into 2 types: ANCA-positive (ANCA+) and ANCA-negative (ANCA–). In the first variant, the phenomena of vasculitis prevail, in the second — mainly allergic symptoms. The main approaches to the treatment of such patients are based on their condition and the risk of mortality. Our clinical observation characterizes the difficulties of diagnosis in patients with systemic vasculitis and shows the possibilities of a multidisciplinary approach in their diagnosis in a multidisciplinary hospital.
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